Rare case of glanzmann thrombastenia.

Abstract

Recurrent Epistaxis often is due to thrombocytopenia. Child with recurrent Epistaxis had abnormal bleeding time, coupled with normal platelet count congenital Glanzmann Thrombasthenia (GT) though rare is a possible condition. Severe bleeding in GT required platelet transfusions, and whole blood (as replacement for gross blood loss). Suspect Glanzmann Thrombasthenia, when recurrent Epistaxis with prolonged bleeding time is associated with normal platelet count. Mild bleeding is best treated with local and IV Tranexamic acid (30 mg / kg).